Ultrasound Diagnosis of Mayer-Rokitansky-Küster-Hauser Syndrome in a Resource-Limited Setting: A Case Report from Nigeria
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Abstract
Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is a congenital Müllerian anomaly and an important cause of primary amenorrhea. We report a 27-year-old Nigerian woman with normal secondary sexual characteristics. Transabdominal pelvic ultrasound showed complete uterine agenesis, with normal bilateral ovaries and kidneys, consistent with type I MRKH syndrome. This case demonstrates that ultrasound can provide a reliable, accessible, and affordable diagnosis in resource-limited settings where magnetic resonance imaging is unavailable or unaffordable, enabling timely counseling, psychological support, and multidisciplinary management.
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